{"id":19388,"date":"2025-02-04T15:36:50","date_gmt":"2025-02-04T15:36:50","guid":{"rendered":"https:\/\/www.mizuho.kr\/?p=5099"},"modified":"2026-09-06T04:47:23","modified_gmt":"2026-09-05T19:47:23","slug":"alpha-mannosidosis-treatment-market-datam","status":"publish","type":"post","link":"https:\/\/www.globalresearch.co.kr\/insight\/alpha-mannosidosis-treatment-market-datam\/","title":{"rendered":"\uae00\ub85c\ubc8c \uc54c\ud30c-\ub9cc\ub178\uc2dc\ub3c4\uc99d \uc2dc\uc7a5 : \uc801\uc751\uc99d\ubcc4 (\uc720\ud615 I, \uc720\ud615 II, \uc720\ud615 III)"},"content":{"rendered":"

\"\"<\/p>\n

 <\/p>\n

    \n
  1. \ubc29\ubc95\ub860 \ubc0f \ubc94\uc704<\/b>\n
      \n
    1. \uc5f0\uad6c \ubc29\ubc95\ub860<\/li>\n
    2. \ubcf4\uace0\uc11c\uc758 \uc5f0\uad6c \ubaa9\uc801 \ubc0f \ubc94\uc704<\/li>\n<\/ol>\n<\/li>\n
    3. \uc815\uc758 \ubc0f \uac1c\uc694<\/b><\/li>\n
    4. \uc784\uc6d0 \uc694\uc57d<\/b>\n
        \n
      1. \uc801\uc751\uc99d\ubcc4 \uc2a4\ub2c8\ud3ab<\/li>\n
      2. \uce58\ub8cc\ubcc4 \uc2a4\ub2c8\ud3ab<\/li>\n
      3. \ucd5c\uc885 \uc0ac\uc6a9\uc790\ubcc4 \uc2a4\ub2c8\ud3ab<\/li>\n
      4. \uc9c0\uc5ed\ubcc4 \uc2a4\ub2c8\ud3ab<\/li>\n<\/ol>\n<\/li>\n
      5. \uc2dc\uc7a5 \uc5ed\ud559<\/b>\n
          \n
        1. \uc601\ud5a5 \uc694\uc778\n
            \n
          1. \ub3d9\uc778\n
              \n
            1. \uc815\ubd80 \uae30\uad00\uc758 \uc2b9\uc778 \uc99d\uac00<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n
            2. \uc81c\uc57d \uc694\uc778\n
                \n
              1. \uae30\ud68c<\/li>\n
              2. \uc601\ud5a5 \ubd84\uc11d<\/li>\n
              3. \ud76c\uadc0 \uc9c8\ud658 \uc5f0\uad6c\ub97c \uc704\ud55c \uc81c\ud55c\ub41c \uc790\uae08<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n
              4. \uc0b0\uc5c5 \ubd84\uc11d<\/b>\n
                  \n
                1. \ud3ec\ud130\uc758 \ub2e4\uc12f \uac00\uc9c0 \ud798 \ubd84\uc11d<\/li>\n
                2. \uacf5\uae09\ub9dd \ubd84\uc11d<\/li>\n
                3. \uac00\uaca9 \ubd84\uc11d<\/li>\n
                4. \uaddc\uc81c \ubd84\uc11d<\/li>\n
                5. \ud30c\uc774\ud504\ub77c\uc778 \ubd84\uc11d<\/li>\n
                6. \ucda9\uc871\ub418\uc9c0 \uc54a\uc740 \uc694\uad6c<\/li>\n
                7. DMI \uc758\uacac<\/li>\n<\/ol>\n<\/li>\n
                8. COVID-19 \ubd84\uc11d<\/b>\n
                    \n
                  1. \ucf54\ub85c\ub09819 \ubd84\uc11d\n
                      \n
                    1. \ucf54\ub85c\ub098 \uc774\uc804 \uc2dc\ub098\ub9ac\uc624<\/li>\n
                    2. \ucf54\ub85c\ub09819 \uc911 \uc2dc\ub098\ub9ac\uc624<\/li>\n
                    3. \ucf54\ub85c\ub098 \uc774\ud6c4 \uc2dc\ub098\ub9ac\uc624<\/li>\n<\/ol>\n<\/li>\n
                    4. \ucf54\ub85c\ub09819\uc5d0 \ub530\ub978 \uac00\uaca9 \uc5ed\ud559<\/li>\n
                    5. \uc218\uc694-\uacf5\uae09 \uc2a4\ud399\ud2b8\ub7fc<\/li>\n
                    6. \ud32c\ub370\ubbf9 \uae30\uac04 \uc911 \uc2dc\uc7a5\uacfc \uad00\ub828\ub41c \uc815\ubd80 \uc774\ub2c8\uc154\ud2f0\ube0c<\/li>\n
                    7. \uc81c\uc870\uc5c5\uccb4\uc758 \uc804\ub7b5\uc801 \uc774\ub2c8\uc154\ud2f0\ube0c<\/li>\n
                    8. \uacb0\ub860<\/li>\n<\/ol>\n<\/li>\n
                    9. \uc801\uc751\uc99d\ubcc4<\/b>\n
                        \n
                      1. \uc18c\uac1c\n
                          \n
                        1. \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%), \uc801\uc751\uc99d\ubcc4<\/li>\n
                        2. \uc2dc\uc7a5 \ub9e4\ub825\ub3c4 \uc9c0\uc218, \uc801\uc751\uc99d\ubcc4<\/li>\n<\/ol>\n<\/li>\n
                        3. \uc720\ud615 I *\n
                            \n
                          1. \uc18c\uac1c<\/li>\n
                          2. \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144\ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%)<\/li>\n<\/ol>\n<\/li>\n
                          3. \uc720\ud615 II<\/li>\n
                          4. \uc720\ud615 III<\/li>\n<\/ol>\n<\/li>\n
                          5. \uce58\ub8cc\ubcc4<\/b>\n
                              \n
                            1. \uc18c\uac1c\n
                                \n
                              1. \uce58\ub8cc\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%)<\/li>\n
                              2. \uce58\ub8cc\ubcc4 \uc2dc\uc7a5 \ub9e4\ub825\ub3c4 \uc9c0\uc218<\/li>\n<\/ol>\n<\/li>\n
                              3. \uace8\uc218 \uc774\uc2dd(BMT) *\n
                                  \n
                                1. \uc18c\uac1c<\/li>\n
                                2. \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%)<\/li>\n<\/ol>\n<\/li>\n
                                3. \ud6a8\uc18c \ub300\uccb4 \uc694\ubc95(ERT)<\/li>\n
                                4. \uc720\uc804\uc790 \uce58\ub8cc<\/li>\n
                                5. \uae30\ud0c0<\/li>\n<\/ol>\n<\/li>\n
                                6. \ucd5c\uc885 \uc0ac\uc6a9\uc790\ubcc4<\/b>\n
                                    \n
                                  1. \uc18c\uac1c\n
                                      \n
                                    1. \ucd5c\uc885 \uc0ac\uc6a9\uc790\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%)<\/li>\n
                                    2. \ucd5c\uc885 \uc0ac\uc6a9\uc790\ubcc4 \uc2dc\uc7a5 \ub9e4\ub825\ub3c4 \uc9c0\uc218<\/li>\n<\/ol>\n<\/li>\n
                                    3. \ubcd1\uc6d0*\n
                                        \n
                                      1. \uc18c\uac1c<\/li>\n
                                      2. \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%)<\/li>\n<\/ol>\n<\/li>\n
                                      3. \uc804\ubb38 \ud074\ub9ac\ub2c9<\/li>\n
                                      4. \uae30\ud0c0<\/li>\n<\/ol>\n<\/li>\n
                                      5. \uc9c0\uc5ed\ubcc4<\/b>\n
                                          \n
                                        1. \uc18c\uac1c\n
                                            \n
                                          1. \uc9c0\uc5ed\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%)<\/li>\n
                                          2. \uc9c0\uc5ed\ubcc4 \uc2dc\uc7a5 \ub9e4\ub825\ub3c4 \uc9c0\uc218<\/li>\n<\/ol>\n<\/li>\n
                                          3. \ubd81\ubbf8\n
                                              \n
                                            1. \uc18c\uac1c<\/li>\n
                                            2. \uc8fc\uc694 \uc9c0\uc5ed\ubcc4 \uc5ed\ud559 \uad00\uacc4<\/li>\n
                                            3. \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%), \uc801\uc751\uc99d \ubcc4<\/li>\n
                                            4. \uce58\ub8cc\ubc95 \ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)<\/li>\n
                                            5. \ucd5c\uc885 \uc0ac\uc6a9\uc790 \ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)<\/li>\n
                                            6. \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%), \uad6d\uac00 \ubcc4\n
                                                \n
                                              1. \ubbf8\uad6d<\/li>\n
                                              2. \uce90\ub098\ub2e4<\/li>\n
                                              3. \uba55\uc2dc\ucf54<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n
                                              4. \uc720\ub7fd\n
                                                  \n
                                                1. \uc18c\uac1c<\/li>\n
                                                2. \uc8fc\uc694 \uc9c0\uc5ed\ubcc4 \uc5ed\ud559 \uad00\uacc4<\/li>\n
                                                3. \uc801\uc751\uc99d\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%)<\/li>\n
                                                4. \uce58\ub8cc\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%), \uce58\ub8cc\ubcc4<\/li>\n
                                                5. \ucd5c\uc885 \uc0ac\uc6a9\uc790 \ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)<\/li>\n
                                                6. \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%), \uad6d\uac00 \ubcc4\n
                                                    \n
                                                  1. \ub3c5\uc77c<\/li>\n
                                                  2. \uc601\uad6d<\/li>\n
                                                  3. \ud504\ub791\uc2a4<\/li>\n
                                                  4. \uc774\ud0c8\ub9ac\uc544<\/li>\n
                                                  5. \uc2a4\ud398\uc778<\/li>\n
                                                  6. \uae30\ud0c0 \uc720\ub7fd<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n
                                                  7. \ub0a8\ubbf8\n
                                                      \n
                                                    1. \uc18c\uac1c<\/li>\n
                                                    2. \uc8fc\uc694 \uc9c0\uc5ed\ubcc4 \uc5ed\ud559 \uad00\uacc4<\/li>\n
                                                    3. \uc801\uc751\uc99d\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5\ub960 \ubd84\uc11d(%)<\/li>\n
                                                    4. \uce58\ub8cc\ubc95 \ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)<\/li>\n
                                                    5. \ucd5c\uc885 \uc0ac\uc6a9\uc790 \ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)<\/li>\n
                                                    6. \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%), \uad6d\uac00 \ubcc4\n
                                                        \n
                                                      1. \ube0c\ub77c\uc9c8<\/li>\n
                                                      2. \uc544\ub974\ud5e8\ud2f0\ub098<\/li>\n
                                                      3. \ub098\uba38\uc9c0 \ub0a8\ubbf8<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n
                                                      4. \uc544\uc2dc\uc544 \ud0dc\ud3c9\uc591\n
                                                          \n
                                                        1. \uc18c\uac1c<\/li>\n
                                                        2. \uc8fc\uc694 \uc9c0\uc5ed\ubcc4 \uc5ed\ud559 \uad00\uacc4<\/li>\n
                                                        3. \uc801\uc751\uc99d\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d(%), \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d(%)<\/li>\n
                                                        4. \uce58\ub8cc\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%), \uce58\ub8cc\ubcc4<\/li>\n
                                                        5. \ucd5c\uc885 \uc0ac\uc6a9\uc790 \ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)<\/li>\n
                                                        6. \uad6d\uac00 \ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)\n
                                                            \n
                                                          1. \uc911\uad6d<\/li>\n
                                                          2. \uc778\ub3c4<\/li>\n
                                                          3. \uc77c\ubcf8<\/li>\n
                                                          4. \ud638\uc8fc<\/li>\n
                                                          5. \uae30\ud0c0 \uc544\uc2dc\uc544 \ud0dc\ud3c9\uc591 \uc9c0\uc5ed<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n
                                                          6. \uc911\ub3d9 \ubc0f \uc544\ud504\ub9ac\uce74\n
                                                              \n
                                                            1. \uc18c\uac1c<\/li>\n
                                                            2. \uc8fc\uc694 \uc9c0\uc5ed\ubcc4 \uc5ed\ud559 \uad00\uacc4<\/li>\n
                                                            3. \uc801\uc751\uc99d\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d(%), \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d(%)<\/li>\n
                                                            4. \uce58\ub8cc\ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)<\/li>\n
                                                            5. \ucd5c\uc885 \uc0ac\uc6a9\uc790 \uadf8\ub8f9 \ubcc4 \uc2dc\uc7a5 \uaddc\ubaa8 \ubd84\uc11d \ubc0f \uc804\ub144 \ub300\ube44 \uc131\uc7a5 \ubd84\uc11d (%)<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n
                                                            6. \uacbd\uc7c1 \ud658\uacbd<\/b>\n
                                                                \n
                                                              1. \uacbd\uc7c1 \uc2dc\ub098\ub9ac\uc624<\/li>\n
                                                              2. \uc2dc\uc7a5 \ud3ec\uc9c0\uc154\ub2dd\/\uc810\uc720\uc728 \ubd84\uc11d<\/li>\n
                                                              3. \uc778\uc218\ud569\ubcd1 \ubd84\uc11d<\/li>\n<\/ol>\n<\/li>\n
                                                              4. \uae30\uc5c5 \ud504\ub85c\ud544<\/b><\/li>\n<\/ol>\n

                                                                 <\/p>\n

                                                                \"\"<\/p>\n","protected":false},"excerpt":{"rendered":"

                                                                \uae00\ub85c\ubc8c \uc54c\ud30c \ub9cc\ub178\uc2dc\ub3c4\uc99d \uc2dc\uc7a5\uc740 2023\ub144\uc5d0 \ubbf8\ud654 \ubc31\ub9cc \ub2ec\ub7ec\uc5d0 \ub3c4\ub2ec\ud588\uc73c\uba70 2031\ub144\uc5d0\ub294 \ubbf8\ud654 \ubc31\ub9cc \ub2ec\ub7ec\uc5d0 \ub3c4\ub2ec\ud560 \uac83\uc73c\ub85c \uc608\uc0c1\ub418\uba70, \uc608\uce21 \uae30\uac04 2024-2031\ub144 \ub3d9\uc548 \ubbf8\ud654 \ubc31\ub9cc \ub2ec\ub7ec\uc758 CAGR\ub85c \uc131\uc7a5\ud560 \uac83\uc73c\ub85c \uc608\uc0c1\ub429\ub2c8\ub2e4.
                                                                \n\uc54c\ud30c-\ub9cc\ub178\uc2dc\uc99d\uc740 \uc2e0\uccb4 \uc138\ud3ec\uc5d0\uc11c \ud2b9\uc815 \uadf8\ub8f9\uc758 \ubcf5\ud569 \ub2f9\uc744 \uc81c\ub300\ub85c \ubd84\ud574\ud558\uc9c0 \ubabb\ud558\ub294 \ud76c\uadc0 \uc720\uc804 \uc9c8\ud658\uc785\ub2c8\ub2e4. \uc911\ucd94 \uc2e0\uacbd\uacc4\ub97c \ud3ec\ud568\ud55c \uc218\ub9ce\uc740 \uc2e0\uccb4 \uae30\uad00\uacfc \uc2dc\uc2a4\ud15c\uc774 \ub2f9 \ucd95\uc801\uc758 \uc601\ud5a5\uc744 \ubc1b\uc2b5\ub2c8\ub2e4. \uc774 \uc9c8\ubcd1\uc758 \uc601\ud5a5\uc740 \uc0ac\ub78c\ub9c8\ub2e4 \ud06c\uac8c \ub2e4\ub97c \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uc54c\ud30c \ub9cc\ub178\uc2dc\ub2e4\uc99d\uc740 \uc54c\ud30c \ub9cc\ub178\uc2dc\ub2e4\uc81c \ud6a8\uc18c\uc758 \uc0dd\uc131\uc744 \ucf54\ub529\ud558\ub294 MAN2B1 \uc720\uc804\uc790\uc758 \ubcc0\ud654\ub85c \uc778\ud574 \ubc1c\uc0dd\ud569\ub2c8\ub2e4.
                                                                \n\uc54c\ud30c-\ub9cc\ub178\uc2dc\ub3c4\uc99d \ud658\uc790\uc758 \uc911\uc99d\ub3c4\ub294 \ub2e4\uc591\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \ubc1c\ub2ec \uc9c0\uc5f0, \uc9c0\uc801 \uc7a5\uc560, \uc5b8\uc5b4 \uc7a5\uc560, \uccad\ub825 \uc0c1\uc2e4, \ubf08 \uae30\ud615 \ub4f1\uc774 \ub300\ud45c\uc801\uc778 \uc99d\uc0c1\uc785\ub2c8\ub2e4. \uc54c\ud30c \ub9cc\ub178\uc2dc\ub2e4\uc81c \ud6a8\uc18c \uc0dd\uc0b0\uc5d0 \ub300\ud55c \uc9c0\uce68\uc744 \uc81c\uacf5\ud558\ub294 MAN2B1 \uc720\uc804\uc790\ub294 \uc54c\ud30c \ub9cc\ub178\uc2dc\ub2e4\uc99d\uc5d0\uc11c \ub3cc\uc5f0\ubcc0\uc774\ub97c \uc77c\uc73c\ud0b5\ub2c8\ub2e4. \ud604\uc7ac \uc54c\ud30c \ub9cc\ub178\uc2dc\uc99d\uc5d0 \ub300\ud55c \uce58\ub8cc\ubc95\uc740 \uc5c6\uc73c\uba70, \ub300\uc2e0 \uc99d\uc0c1 \uad00\ub9ac\uc640 \uc9c0\uc9c0 \uce58\ub8cc\uc5d0 \uc911\uc810\uc744 \ub450\uace0 \uc788\uc2b5\ub2c8\ub2e4.<\/p>\n

                                                                \uc2dc\uc7a5 \uc5ed\ud559
                                                                \n\uc81c\uc57d
                                                                \n\uc815\ubd80 \uae30\uad00\uc758 \uc2b9\uc778 \uc99d\uac00
                                                                \n\uc720\ub7fd \uc758\uc57d\ud488\uccad(EMA) \ubc0f \ubbf8\uad6d \uc2dd\ud488\uc758\uc57d\uad6d(FDA)\uacfc \uac19\uc740 \uaddc\uc81c \uae30\uad00\uc740 \ud76c\uadc0\uc9c8\ud658 \uce58\ub8cc\uc81c \uac1c\ubc1c\uc744 \ucd09\uc9c4\ud558\uae30 \uc704\ud55c \uc774\ub2c8\uc154\ud2f0\ube0c\uc640 \uc778\uc13c\ud2f0\ube0c\ub97c \uc81c\uacf5\ud569\ub2c8\ub2e4. \uc774\ub7ec\ud55c \uc774\ub2c8\uc154\ud2f0\ube0c\ub294 \uc5c5\uacc4\uc758 \uc2ec\uce35\uc801\uc778 \uc5f0\uad6c \uac1c\ubc1c\uc744 \ucd09\uc9c4\ud558\ub294 \ub3d9\uc2dc\uc5d0 \uc2dc\uc7a5 \ud655\ub300\ub97c \ub3d5\uc2b5\ub2c8\ub2e4.
                                                                \n\uc608\ub97c \ub4e4\uc5b4, 2023\ub144 2\uc6d4 \ubbf8\uad6d \uc2dd\ud488\uc758\uc57d\uad6d(FDA)\uc740 \uc131\uc778 \ubc0f \uc18c\uc544 \uc54c\ud30c-\ub9cc\ub178\uc2dc\ub3c4\uc99d(AM) \uce58\ub8cc\uc81c\ub85c \ub7a8\uc81c\ub4dc(\ubca8\ub9c8\ub098\uc81c \uc54c\ud30c-\ud2f0\uc528\ube0c)\ub97c \uc2b9\uc778\ud588\ub2e4\uace0 Chiesi Farmaceutici S.p.A.\uc758 \uc0ac\uc5c5\ubd80\uc778 Chiesi Global Rare Diseases\uac00 \ubc1d\ud614\uc2b5\ub2c8\ub2e4. \ud6a8\uc18c-\ub9cc\ub178\uc2dc\ub2e4\uc81c\uac00 \ubd80\uc871\ud558\uba74 \uadf9\ud788 \ub4dc\ubb3c\uace0 \uc9c4\ud589\ub418\ub294 \ub9ac\uc18c\uc880 \uc800\uc7a5 \uc7a5\uc560\uc778 AM\uc774 \ubc1c\uc0dd\ud569\ub2c8\ub2e4.
                                                                \n\uc720\uc804\ud559 \ubc0f \ubd84\uc790\uc0dd\ubb3c\ud559\uc744 \ud3ec\ud568\ud55c \uc758\ud559\uc758 \uc9c0\uc18d\uc801\uc778 \ubc1c\uc804\uc73c\ub85c \uc778\ud574 \uc774 \uc9c8\ud658\uc758 \uba54\ucee4\ub2c8\uc998\uc774 \uc798 \uc815\uc758\ub418\uace0 \uc788\uc2b5\ub2c8\ub2e4. \uc774\ub7ec\ud55c \uc815\ubcf4\ub97c \ubc14\ud0d5\uc73c\ub85c \ud45c\uc801 \uce58\ub8cc\uc81c\ub97c \uac1c\ubc1c\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uc81c\uc57d \ud68c\uc0ac, \uc0dd\uba85\uacf5\ud559 \ud68c\uc0ac, \uc5f0\uad6c \uae30\uad00\uc5d0\uc11c \ud76c\uadc0 \uc9c8\ud658 \uce58\ub8cc\uc81c\ub97c \uac1c\ubc1c\ud558\uae30 \uc704\ud574 \ub9ce\uc740 \ud22c\uc790\ub97c \ud558\uace0 \uc788\uc2b5\ub2c8\ub2e4. \ud601\uc2e0\uc801\uc778 \uce58\ub8cc\ubc95\uc744 \uc2dc\uc7a5\uc5d0 \ucd9c\uc2dc\ud558\uae30 \uc704\ud574 \uc790\uae08\uacfc \ud22c\uc790\ub294 \uc5f0\uad6c \ud504\ub85c\uc138\uc2a4\ub97c \uac00\uc18d\ud654\ud558\uace0 \uc784\uc0c1\uc2dc\ud5d8\uc744 \ub354 \ube60\ub974\uac8c \uc9c4\ud589\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4.
                                                                \n\uc81c\uc57d
                                                                \n\uc54c\ud30c-\ub9cc\ub178\uc2dc\ub4dc\uc99d\uc758 \uad00\ub9ac\uc640 \uce58\ub8cc\ub97c \uc81c\ud55c\ud560 \uc218 \uc788\ub294 \uba87 \uac00\uc9c0 \uc694\uc778\uc774 \uc788\uc2b5\ub2c8\ub2e4. \uc608\ub97c \ub4e4\uc5b4, \uc720\ub9dd\ud55c \uce58\ub8cc\ubc95\uc774 \uac1c\ubc1c\ub418\ub354\ub77c\ub3c4 \ud2b9\ud788 \uc758\ub8cc \uc790\uc6d0\uc774 \uc81c\ud55c\uc801\uc774\uac70\ub098 \uacbd\uc81c\uc801\uc73c\ub85c \ucde8\uc57d\ud55c \uc9c0\uc5ed\uc5d0\uc11c\ub294 \uad11\ubc94\uc704\ud55c \uc811\uadfc\uc131\uc744 \ubcf4\uc7a5\ud558\uae30 \uc5b4\ub824\uc6b8 \uc218 \uc788\uc73c\uba70, \ud76c\uadc0 \uc9c8\ud658 \uc5f0\uad6c\uc5d0 \ub300\ud55c \uc81c\ud55c\ub41c \uc790\uae08\uc774 \uc774\ub97c \ubc29\ud574\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uc54c\ud30c-\ub9cc\ub178\uc2dc\uc99d\uc740 \ud76c\uadc0\uc131\uacfc \uc99d\uc0c1\uc758 \ub2e4\uc591\uc131\uc73c\ub85c \uc778\ud574 \uc9c4\ub2e8\uc774 \uc5b4\ub824\uc6b8 \uc218 \uc788\uc73c\uba70, \uc624\uc9c4 \ub610\ub294 \ubbf8\uc9c4\ub2e8\uc73c\ub85c \uc778\ud574 \uc801\uc808\ud55c \uc758\ub8cc \uad00\ub9ac\uac00 \uc9c0\uc5f0\ub420 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uc2dc\uc7a5 \uaddc\ubaa8\uac00 \uc791\uae30 \ub54c\ubb38\uc5d0 \uc81c\uc57d \ud68c\uc0ac\ub294 \ud76c\uadc0 \uc9c8\ud658 \uce58\ub8cc\uc81c\uc5d0 \ub300\ud55c \ud22c\uc790 \ub3d9\uae30\uac00 \ub5a8\uc5b4\uc9c8 \uc218 \uc788\uc2b5\ub2c8\ub2e4.
                                                                \n\uc2dc\uc7a5 \uc138\ubd84\ud654 \ubd84\uc11d
                                                                \n\uae00\ub85c\ubc8c \uc54c\ud30c \ub9cc\ub178\uc2dc\uc99d \uc2dc\uc7a5\uc740 \uc801\uc751\uc99d, \uce58\ub8cc\ubc95, \ucd5c\uc885 \uc0ac\uc6a9\uc790 \ubc0f \uc9c0\uc5ed\uc5d0 \ub530\ub77c \uc138\ubd84\ud654\ub429\ub2c8\ub2e4.
                                                                \n\uc720\ud615 \uc138\uadf8\uba3c\ud2b8\uc5d0\uc11c \ud6a8\uc18c \ub300\uccb4 \uc694\ubc95 (ERT) \uc138\uadf8\uba3c\ud2b8\ub294 \uc54c\ud30c-\ub9cc\ub178\uc2dc \uc99d \uc810\uc720\uc728\uc758 \uc57d 39.07 %\ub97c \ucc28\uc9c0\ud588\uc2b5\ub2c8\ub2e4.
                                                                \n\uc54c\ud30c-\ub9cc\ub178\uc2dc\uc99d\uacfc \uac19\uc740 \ud2b9\uc815 \ub9ac\uc18c\uc880 \uc800\uc7a5 \uc7a5\uc560\ub294 \ud6a8\uc18c \ub300\uccb4 \uc694\ubc95 (ERT)\uc73c\ub85c \uc758\ud559\uc801\uc73c\ub85c \uce58\ub8cc\ub429\ub2c8\ub2e4. \uc54c\ud30c-\ub9cc\ub178\uc2dc\ub2e4\uc81c \ud6a8\uc18c\uac00 \ubd80\uc871\ud558\uba74 \uc54c\ud30c-\ub9cc\ub178\uc2dc\ub2e4\uc99d\uc73c\ub85c \uc54c\ub824\uc9c4 \ud76c\uadc0 \uc720\uc804\uc131 \uc9c8\ud658\uc774 \ubc1c\uc0dd\ud569\ub2c8\ub2e4. \uc774\ud6c4 \ud658\uc790\ub294 \ubcd1\uc6d0\uc774\ub098 \uc804\ubb38 \uce58\ub8cc \uc2dc\uc124\uacfc \uac19\uc740 \uc784\uc0c1 \ud658\uacbd\uc5d0\uc11c \uc77c\uc0c1\uc801\uc778 \uc815\ub9e5 \uc8fc\uc0ac\ub97c \ud1b5\ud574 \uc815\uc81c\ub418\uace0 \ubcc0\ud615\ub41c \ud6a8\uc18c\ub97c \ud22c\uc5ec\ubc1b\uac8c \ub429\ub2c8\ub2e4. \ubcf5\ud569 \ud0c4\uc218\ud654\ubb3c\uc740 \uc138\ud3ec\uc758 \ub9ac\uc18c\uc880\uc5d0\uc11c \uc774 \ud6a8\uc18c\uc5d0 \uc758\ud574 \ubd84\ud574\ub418\uc5b4\uc57c \ud569\ub2c8\ub2e4.
                                                                \nERT\ub294 \ud3c9\uc0dd \uce58\ub8cc\uac00 \ud544\uc694\ud55c \uacbd\uc6b0\uac00 \ub9ce\ub2e4\ub294 \uc810\uc744 \uba85\uc2ec\ud558\ub294 \uac83\uc774 \uc911\uc694\ud569\ub2c8\ub2e4. \uccb4\ub0b4 \ud6a8\uc18c \uc218\uce58\ub97c \uc548\uc815\uc801\uc73c\ub85c \uc720\uc9c0\ud558\uace0 \uc800\uc7a5\ub41c \ubb3c\uc9c8\uc758 \ubd84\ud574\ub97c \uacc4\uc18d \uc9c4\ud589\ud558\ub824\uba74 \uc815\uae30\uc801\uc778 \uc218\uc561 \uc8fc\uc785\uc774 \ud544\uc694\ud569\ub2c8\ub2e4. \uc758\ub8cc\uc9c4\uc740 ERT\ub97c \ubc1b\ub294 \ud658\uc790\ub97c \uc815\uae30\uc801\uc73c\ub85c \ubaa8\ub2c8\ud130\ub9c1\ud569\ub2c8\ub2e4. \ud658\uc790\uc758 \ubc18\uc751\uacfc \ud2b9\uc815 \uc694\uad6c \uc0ac\ud56d\uc5d0 \ub530\ub77c \uc8fc\uc785 \uc6a9\ub7c9\uacfc \ube48\ub3c4\ub97c \ubcc0\uacbd\ud574\uc57c \ud560 \uc218\ub3c4 \uc788\uc2b5\ub2c8\ub2e4.
                                                                \n\uc2dc\uc7a5 \uc9c0\ub9ac\uc801 \uc810\uc720\uc728
                                                                \n\ubd81\ubbf8\ub294 2023\ub144 \uc2dc\uc7a5 \uc810\uc720\uc728\uc758 \uc57d 34.04%\ub97c \ucc28\uc9c0\ud588\uc2b5\ub2c8\ub2e4.
                                                                \n\uc54c\ud30c \ub9cc\ub178\uc2dc\uc99d\uc5d0 \ub300\ud55c \uac00\uc7a5 \ud070 \uc2dc\uc7a5 \uc810\uc720\uc728\uc740 \ubd81\ubbf8\uac00 \ucc28\uc9c0\ud588\uc73c\uba70, \uadf8 \uc6b0\uc704\ub294 \uc8fc\ub85c \ubd81\ubbf8\uc5d0\uc11c \uc218\ud589 \ub41c \uc784\uc0c1 \uc2dc\ud5d8\uc758 \ub354 \ub9ce\uc740 \uc591\uc73c\ub85c \uc124\uba85\ub418\uc5c8\uc2b5\ub2c8\ub2e4. \ub610\ud55c, \uc774 \uc9c0\uc5ed\uc740 \ud76c\uadc0 \uc758\uc57d\ud488 \uac1c\ubc1c\uc774 \uc99d\uac00\ud558\uace0 \uc788\uc2b5\ub2c8\ub2e4. \uc774\ub7ec\ud55c \uc815\ubd80 \uc815\ucc45\uc758 \uacb0\uacfc\ub85c \ub9ce\uc740 \ud76c\uadc0 \uc758\uc57d\ud488\uc774 FDA \ubc0f \uae30\ud0c0 \uaddc\uc81c \uae30\uad00\uc758 \uc2b9\uc778\uc744 \ubc1b\uace0 \uc788\uc2b5\ub2c8\ub2e4.
                                                                \n\ub610\ud55c \uc9c0\uc5ed \uc911\uc5d0\uc11c\ub294 \uc720\ub7fd\uc758 \ub9cc\ub178\uc2dc\uc99d \uc2dc\uc7a5\uc774 \uac00\uc7a5 \ube60\ub978 \uc18d\ub3c4\ub85c \uc131\uc7a5\ud560 \uac83\uc73c\ub85c \uc608\uc0c1\ub429\ub2c8\ub2e4. \ud76c\uadc0 \uc720\uc804 \uc9c8\ud658\uacfc \uad00\ub828 \uce58\ub8cc\ubc95\uc5d0 \ub300\ud55c \ub300\uc911\uc758 \uc778\uc2dd\uc744 \ub192\uc774\uae30 \uc704\ud55c \uc815\ubd80\uc758 \ub2e4\uc591\ud55c \uc2dc\ub3c4\uac00 \uc720\ub7fd\uc5d0\uc11c \uc2dc\uc7a5 \ud655\ub300\uc5d0 \uc601\ud5a5\uc744 \ubbf8\ucce4\uc2b5\ub2c8\ub2e4.
                                                                \n\ucf54\ub85c\ub09819 \uc601\ud5a5 \ubd84\uc11d
                                                                \n\uc2e0\uc885 \ucf54\ub85c\ub098\ubc14\uc774\ub7ec\uc2a4\uc758 \ud655\uc0b0\uc740 \ub2e8\uae30\uac04\uc5d0 \uc804 \uc138\uacc4 \uc54c\ud30c \ub9cc\ub178\uc2dc\uc99d \uc2dc\uc7a5\uc5d0 \ub2e4\uc18c \uc545\uc601\ud5a5\uc744 \ubbf8\ucce4\uc2b5\ub2c8\ub2e4. \ud32c\ub370\ubbf9 \uae30\uac04 \ub3d9\uc548 \uc758\ub8cc, \uc81c\uc57d \ubc0f \uae30\ud0c0 \uad00\ub828 \uc0b0\uc5c5\uc740 \uadf9\uc2ec\ud55c \uc555\ubc15\uc744 \ubc1b\uc558\uc2b5\ub2c8\ub2e4. \ucf54\ub85c\ub09819 \ud658\uc790 \uc218\ub294 \ubcd1\uc6d0\uacfc \uc9c4\ub8cc\uc18c\uac00 \ub118\uccd0\ub0a0 \uc815\ub3c4\ub85c \uc99d\uac00\ud588\uc2b5\ub2c8\ub2e4. \uc774\ub7ec\ud55c \uc2dc\uc124\uc758 \uc790\uc6d0\uc740 \uac70\uc758 \uc804\uc801\uc73c\ub85c \ud32c\ub370\ubbf9\uacfc \uc2f8\uc6b0\ub294 \ub370 \ud22c\uc785\ub418\uc5c8\uc2b5\ub2c8\ub2e4. \uc774\ub85c \uc778\ud574 \uc54c\ud30c \ub9cc\ub178\uc2dc\uc99d\uacfc \uac19\uc740 \uc720\uc804 \uc9c8\ud658\uacfc \uac19\uc774 \ub35c \uc2ec\uac01\ud55c \ub2e4\ub978 \uc9c8\ubcd1\uc744 \uc553\uace0 \uc788\ub294 \uc0ac\ub78c\ub4e4\uc744 \ubc29\uce58\ud558\ub294 \uacb0\uacfc\ub97c \ucd08\ub798\ud588\uc2b5\ub2c8\ub2e4.
                                                                \n\ub610\ud55c \ub9ce\uc740 \uc815\ubd80 \ubc0f \ubbfc\uac04 \uc758\ub8cc \uae30\uad00\uc774 \ud32c\ub370\ubbf9 \uc704\uae30 \ub300\uc751\uc5d0 \uc6b0\uc120\uc21c\uc704\ub97c \ub450\uc5c8\uc2b5\ub2c8\ub2e4. \uc774\ub85c \uc778\ud574 \ucf54\ub85c\ub09819 \uc774\uc678\uc758 \uc9c8\ubcd1\uc5d0 \uc0ac\uc6a9\ud560 \uc218 \uc788\ub294 \uc790\uae08\uc774 \uc904\uc5b4\ub4e4\uc5c8\uc2b5\ub2c8\ub2e4. \uc758\ub8cc \uc11c\ube44\uc2a4 \uc81c\uacf5\uc790\ub4e4\uc740 \ucf54\ub85c\ub09819 \ud655\uc9c4\uc790 \uc218\uac00 \uac10\uc18c\ud568\uc5d0 \ub530\ub77c \ub2e4\ub978 \uac74\uac15 \uc0c1\ud0dc\ub97c \uac00\uc9c4 \ube44\ucf54\ub85c\ub098 \ud658\uc790\ub4e4\uc5d0\uac8c \uc9d1\uc911\ud560 \uac83\uc73c\ub85c \uc608\uc0c1\ub429\ub2c8\ub2e4. \uc774\uc5d0 \ub530\ub77c \ud32c\ub370\ubbf9 \uc774\ud6c4 \uae30\uac04 \ub3d9\uc548 \uc2dc\uc7a5 \ud655\ub300\uac00 \uac00\uc18d\ud654\ub420 \uac83\uc73c\ub85c \uc608\uc0c1\ub429\ub2c8\ub2e4.<\/p>\n

                                                                \ubcf4\uace0\uc11c\ub97c \uad6c\ub9e4\ud558\ub294 \uc774\uc720\ub294 \ubb34\uc5c7\uc785\ub2c8\uae4c?
                                                                \n\uc801\uc751\uc99d, \uce58\ub8cc, \ucd5c\uc885 \uc0ac\uc6a9\uc790 \ubc0f \uc9c0\uc5ed\uc744 \uae30\ubc18\uc73c\ub85c \uae00\ub85c\ubc8c \uc54c\ud30c-\ub9cc\ub178\uc2dc\ub3c4\uc99d \uc2dc\uc7a5 \uc138\ubd84\ud654\ub97c \uc2dc\uac01\ud654\ud558\uace0 \uc8fc\uc694 \uc0c1\uc5c5 \uc790\uc0b0 \ubc0f \ud50c\ub808\uc774\uc5b4\ub97c \uc774\ud574\ud569\ub2c8\ub2e4.
                                                                \n\ud2b8\ub80c\ub4dc\uc640 \uacf5\ub3d9 \uac1c\ubc1c\uc744 \ubd84\uc11d\ud558\uc5ec \uc0c1\uc5c5\uc801 \uae30\ud68c\ub97c \ud30c\uc545\ud569\ub2c8\ub2e4.
                                                                \n\ubaa8\ub4e0 \uc138\uadf8\uba3c\ud2b8\uc5d0 \ub300\ud55c \uc54c\ud30c-\ub9cc\ub178\uc2dc\ub3c4\uc99d \uc2dc\uc7a5 \uc218\uc900\uc758 \uc218\ub9ce\uc740 \ub370\uc774\ud130 \ud3ec\uc778\ud2b8\uac00 \ud3ec\ud568\ub41c Excel \ub370\uc774\ud130 \uc2dc\ud2b8.
                                                                \nPDF \ubcf4\uace0\uc11c\ub294 \ucca0\uc800\ud55c \uc815\uc131\uc801 \uc778\ud130\ubdf0\uc640 \uc2ec\uce35 \uc5f0\uad6c\ub97c \uac70\uce5c \uc885\ud569\uc801\uc778 \ubd84\uc11d\uc73c\ub85c \uad6c\uc131\ub429\ub2c8\ub2e4.
                                                                \n\ubaa8\ub4e0 \uc8fc\uc694 \uc5c5\uccb4\uc758 \uc8fc\uc694 \uc81c\ud488\uc73c\ub85c \uad6c\uc131\ub41c \uc81c\ud488 \ub9e4\ud551\uc744 \uc5d1\uc140\ub85c \uc81c\uacf5\ud569\ub2c8\ub2e4.<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[5],"tags":[],"class_list":["post-19388","post","type-post","status-publish","format-standard","hentry","category-industry-research-report"],"_links":{"self":[{"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/posts\/19388"}],"collection":[{"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/comments?post=19388"}],"version-history":[{"count":0,"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/posts\/19388\/revisions"}],"wp:attachment":[{"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/media?parent=19388"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/categories?post=19388"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.globalresearch.co.kr\/insight\/wp-json\/wp\/v2\/tags?post=19388"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}